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IRVAN syndrome in short
- A rare retinal vascular disorder characterized by idiopathic retinal vasculitis, aneurysmal dilations at arteriolar bifurcation points, and neuroretinitis.
- If left untreated, the condition may advance to peripheral capillary non-perfusion, retinal neovascularization, and macular exudation, ultimately resulting in severe bilateral vision loss.
Synonym
- Idiopathic retinal vasculitis-aneurysms-neuroretinitis syndrome
Prevalence: <1 / 1 000 000
Inheritance: Not applicable
Age of onset: Adolescent, Adult, Childhood
What are the symptoms of IRVAN syndrome?
Frequent symptoms
- Ocular hypertension
- Reduced visual acuity
- Vitreous floaters
Occasional symptoms
- Blurred vision
- Glaucoma
- Macular edema
- Optic atrophy
- Photophobia
- Retinal detachment
- Retinal exudate
- Tractional retinal detachment
