Idiopathic inflammatory myopathies classification
How are the idiopathic inflammatory myopathies classified?
Although several classification schemes have been devised, none are perfect. Each IIM and its subsets are characterized by unique clinical features (muscle, skin, lung, other), histology, autoantibodies, and pathogenesis. In addition, some patients may present with a clinical manifestation (rash, ILD, arthritis) that is more predominant than the inflammatory myositis.
- 1. Adult-onset DM
- • DM
- • Amyotrophic DM
- 2. Overlap myositis
- • ASA
- • Myositis associated with other connective tissue diseases
- 3. Adult-onset PM
- 4. Immune-mediated necrotizing myositis (IMNM)
- 5. IBM
- 6. Juvenile-onset DM (JDM)
Some classification systems add the following to the earlier list of inflammatory diseases of the muscle:
- • Other forms of inflammatory myopathy
- – Myositis associated with eosinophilia
- – Focal myositis
- – Giant cell myositis
