What is AIDS cholangiopathy? How do patients present?
AIDS cholangiopathy is a spectrum of biliary tract abnormalities resembling sclerosing cholangitis that can be caused by a wide array of microorganisms and neoplasms, usually in patients with advanced immunodeficiency (CD4 count < 100 cells/mL). Patients generally present with epigastric or right upper quadrant pain, fever, and malaise. Although AIDS cholangiopathy is a cholestatic disease, jaundice and pruritus are uncommon.