How is juvenile dermatomyositis different from adult dermatomyositis or polymyositis?
In children:
- • Dermatomyositis is distinguished by being a generalized vasculitis.
- • Polymyositis is exceedingly rare in childhood. In a child with progressive weakness, other muscle diseases are more likely than polymyositis.
- • Unlike adults, malignancy is rarely associated with childhood dermatomyositis.