What is the difference between TAPVR and scimitar syndrome?
In TAPVR, all of the pulmonary veins empty into the systemic venous circulation instead of the left atrium, creating increased pulmonary blood flow and cyanosis. Scimitar syndrome, or pulmonary venolobar syndrome, is considered to be a type of PAPVR. A characteristic “scimitar” sign is seen on a chest radiograph, where a curvilinear opacity due to an anomalous right pulmonary vein extends inferiorly to the cardiophrenic angle to drain into the inferior vena cava or other systemic venous structure
