International Chapel Hill consensus conference nomenclature for the vasculitides

What is the international Chapel Hill consensus conference nomenclature for the vasculitides?

Here is the table which describes the vasculitis nomenclature agreed at the Chapel Hill consensus conference.

Vasculitis Nomenclature Agreed at the International Chapel Hill Consensus Conference

Large-vessel vasculitisTakayasu arteritis
Giant cell (temporal) arteritis
Medium-vessel vasculitisPolyarteritis nodosa
Kawasaki disease
Small-vessel vasculitisImmune complex-mediated
Antiglomerular basement membrane disease (Goodpasture syndrome)
Cryoglobulinemic vasculitis
IgA vasculitis (Henoch–Schönlein purpura)
Hypocomplementemic urticarial vasculitis (anti-Clq vasculitis)
Antineutrophil cytoplasmic antibody (ANCA)-associated (pauci-immune)
Granulomatosis with polyangiitis (Wegener’s granulomatosis)
Microscopic polyangiitis
Eosinophilic granulomatosis with polyangiitis (Churg–Strauss)
Variable-vessel vasculitis aBehçet disease
Cogan syndrome
Single-organ vasculitisCutaneous leukocytoclastic vasculitis
Cutaneous arteritis
Primary central nervous system vasculitis (isolated angiitis of central nervous system)
Isolated aortitis
Vasculitis associated with systemic diseaseLupus vasculitis
Rheumatoid vasculitis
Sarcoid vasculitis
Vasculitis associated with probable etiologyHepatitis C virus-associated cryoglobulinemic vasculitis
Hepatitis B virus-associated vasculitis
Syphilis-associated vasculitis
Drug-associated immune complex vasculitis (hypersensitivity vasculitis)
Drug-associated ANCA-associated vasculitis
Cancer-associated vasculitis

a Thromboangiitis obliterans (Buerger disease) was not classified at this conference but probably best fits as variable-vessel vasculitis.

Note: There are specific American College of Rheumatology classification criteria for many of the major types of vasculitis. These differentiate one vasculitis from another, rather than describing all of the manifestations of a particular form of vasculitis. Thus, these criteria are rarely useful for diagnosis, and appropriate tissue biopsy is generally necessary for confirmation.


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