What is the international Chapel Hill consensus conference nomenclature for the vasculitides?
Here is the table which describes the vasculitis nomenclature agreed at the Chapel Hill consensus conference.
Vasculitis Nomenclature Agreed at the International Chapel Hill Consensus Conference
| Nomenclature | Vasculitis |
|---|---|
| Large-vessel vasculitis | Takayasu arteritis |
| Giant cell (temporal) arteritis | |
| Medium-vessel vasculitis | Polyarteritis nodosa |
| Kawasaki disease | |
| Small-vessel vasculitis | Immune complex-mediated |
| Antiglomerular basement membrane disease (Goodpasture syndrome) | |
| Cryoglobulinemic vasculitis | |
| IgA vasculitis (Henoch–Schönlein purpura) | |
| Hypocomplementemic urticarial vasculitis (anti-Clq vasculitis) | |
| Antineutrophil cytoplasmic antibody (ANCA)-associated (pauci-immune) | |
| Granulomatosis with polyangiitis (Wegener’s granulomatosis) | |
| Microscopic polyangiitis | |
| Eosinophilic granulomatosis with polyangiitis (Churg–Strauss) | |
| Variable-vessel vasculitis a | Behçet disease |
| Cogan syndrome | |
| Single-organ vasculitis | Cutaneous leukocytoclastic vasculitis |
| Cutaneous arteritis | |
| Primary central nervous system vasculitis (isolated angiitis of central nervous system) | |
| Isolated aortitis | |
| Others | |
| Vasculitis associated with systemic disease | Lupus vasculitis |
| Rheumatoid vasculitis | |
| Sarcoid vasculitis | |
| Others | |
| Vasculitis associated with probable etiology | Hepatitis C virus-associated cryoglobulinemic vasculitis |
| Hepatitis B virus-associated vasculitis | |
| Syphilis-associated vasculitis | |
| Drug-associated immune complex vasculitis (hypersensitivity vasculitis) | |
| Drug-associated ANCA-associated vasculitis | |
| Cancer-associated vasculitis | |
| Others |
a Thromboangiitis obliterans (Buerger disease) was not classified at this conference but probably best fits as variable-vessel vasculitis.
Note: There are specific American College of Rheumatology classification criteria for many of the major types of vasculitis. These differentiate one vasculitis from another, rather than describing all of the manifestations of a particular form of vasculitis. Thus, these criteria are rarely useful for diagnosis, and appropriate tissue biopsy is generally necessary for confirmation.
