Hypoplastic left heart syndrome
In Hypoplastic left heart syndrome, the left-sided cardiac structures (usually the left ventricle and aortic root) are hypoplastic. The right ventricle is surgically recruited to become the systemic pumping ventricle. A neoaortic root is fashioned from the pulmonary outflow track and anastomosed to the aortic arch, an atrial septectomy is performed, and a shunt is temporarily created between the subclavian artery and pulmonary arteries (Norwood procedure). Systemic venous return is subsequently diverted directly to the branch pulmonary arteries through a Glenn procedure (superior vena cava to pulmonary arteries) and a Fontan completion (inferior vena cava to pulmonary arteries.)
