What disorders with adolescent or early adult onset can then present with dementia at a later age?
These include:
- Sphingolipidoses:
- • Adult GM2 gangliosidosis/Tay–Sachs disease
- • Adult GM1 gangliosidosis
- • Adult (type 3) Gaucher’s disease
- • Adult Fabry’s disease
- Adult neuronal ceroid lipofuscinosis/Kuf’s disease
- Adult Leigh’s disease
- Late-onset globoid cell leukodystrophy/Krabbe’s disease
- Adrenoleukodystrophy