Differential Diagnosis of Immune Complex Mediated Small Vessel Vasculitides
What diseases can mimic SVV?
• Pigmented purpuric dermatoses (including conditions such as Schamberg’s disease).
• Antiphospholipid syndrome.
• Livedoid vasculopathy (atrophie blanche)
• Cholesterol emboli.
• Low platelet count: immune thrombocytopenia purpura, thrombotic thrombocytopenic purpura, disseminated intravascular coagulation.
• Meningococcemia.
• Calciphylaxis.
• Infective endocarditis.
• Atrial myxoma.
• Scurvy.
• Amyloidosis.