Differential Diagnosis of Immune Complex Mediated Small Vessel Vasculitides

Differential Diagnosis of Immune Complex Mediated Small Vessel Vasculitides

What diseases can mimic SVV?

• Pigmented purpuric dermatoses (including conditions such as Schamberg’s disease).

• Antiphospholipid syndrome.

• Livedoid vasculopathy (atrophie blanche)

• Cholesterol emboli.

• Low platelet count: immune thrombocytopenia purpura, thrombotic thrombocytopenic purpura, disseminated intravascular coagulation.

• Meningococcemia.

• Calciphylaxis.

• Infective endocarditis.

• Atrial myxoma.

• Scurvy.

• Amyloidosis.

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